What is Polands Syndrome?
Poland syndrome is a rare developmental disorder (1 in 20,000 live births) which is present at birth (congenital). It consists of underdevelopment of some or all of the chest, shoulder and upper limb on one side of the body. The hand difference, if present, is a form of Symbrachydactyly. It affects males more frequently than females.
What causes Polands Syndrome?
The cause of Poland syndrome is thought to be due to a temporary alteration in blood flow in the developing shoulder girdle and upper limb during pregnancy at approximately seven weeks. Individuals affected by Poland syndrome will lead a normal and healthy life.
How is Polands Syndrome treated?
Each case is assessed individually. Hand problems, as well as underdevelopment of the chest and breast can be reconstructed, usually by plastic surgeons.